Май/Июнь 2013, том 3, номер 3

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■ Обзоры литературы

Майданник В.Г. Современные аспекты синдрома периодической лихорадки с афтозным стоматитом, фарингитом и шейным лимфаденитом (синдром Маршалла) у детей. Международный журнал педиатрии, акушерства и гинекологии 2013;Т3(3):63-74

Современные аспекты синдрома периодической лихорадки с афтозным стоматитом, фарингитом и шейным лимфаденитом (синдром Маршалла) у детей

Майданник В.Г.

Национальный медицинский университет имени А.А. Богомольца, Киев, Украина

полный текст (pdf)

■ Резюме:

Синдром Маршалла является довольно распространенным состоянием в детском возрасте, но его этиология и патогенез до сих пор не известны. Считают, что синдром Маршалла является аутовоспалительным заболеванием неизвестной этиологии. Он характеризуется эпизодами лихорадки, продолжающимися 3-6 дней с повторением каждые 3-8 недель, связанные хотя бы с одним из трех основных признаков: афтозный стоматит, шейный лимфаденит и фарингит. Возникновение заболевания обычно происходит в возрасте до 5 лет и, как правило, разрешается в подростковом возрасте. Поскольку эта болезнь доброкачественна и имеет склонность к самоизлечению, лечение должно быть ограничено глюкокортикоидами или другими симптоматическими жаропонижающими препаратами. Тонзиллэктомия может быть использована только для пациентов, резистентных к медикаментозному лечению.

■ Ключевые слова:

периодическая лихорадка, синдром Маршалла, аутовоспалительные синдромы, низкие дозы стероидов, тонзиллэктомия.

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